Posterior polymorphous corneal dystrophy 1
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| Posterior polymorphous corneal dystrophy 1 | |
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| Classification and external resources | |
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File:Posterior polymorphous corneal dystrophy 1.JPEG Appearance of the abnormal corneal endothelial cells that have become transformed into stratified squamous epithelium. Periodic acid Schiff stain | |
| OMIM | 122000 |
Posterior Polymorphous Corneal Dystrophy 1 (PPCD1; sometimes also Schlichting dystrophy) is a rare disease of the cornea, characterised by changes in Descemet's membrane and endothelial layer. Symptoms mainly consist of decreased vision due to corneal edema. In some cases they are present from birth, other patients are asymptomatic. Histopathological analysis shows that the cells of endothelium have some characteristics of epithelial cells, and endothelium itself sometimes consists of more than one cell layer. The disease was first described in 1916 by Koeppe as keratitis bullosa interna.[1]
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See also
References
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<references />, or <references group="..." />External links
- Posterior Polymorphous Corneal Dystrophy at eMedicine
- CORNEAL DYSTROPHY, POSTERIOR POLYMORPHOUS, 1; PPCD1 - OMIMru:Задняя полиморфная дистрофия роговицы, тип 1
- ↑ Klinische Beobachtungen mit der Nernstspaltlampe und dem Hornhautmikroskop. Albrecht von Graefes Arch. Klin. Exp. Ophthal. 91: 363-379, 1916
